"sequence_id","alias","species","description","type" "AFR93224","No alias","Cryptococcus neoformans","mitochondrial intermediate peptidase 2;Peptidase family M3","protein_coding" "AFR93435","No alias","Cryptococcus neoformans","endothelin-converting enzyme;Peptidase family M13","protein_coding" "AFR93532","No alias","Cryptococcus neoformans","AFG3 family protein;ATPase family associated with various cellular activities (AAA);AAA+ lid domain;FtsH Extracellular;Peptidase family M41","protein_coding" "AFR93949","No alias","Cryptococcus neoformans","mitochondrial intermediate peptidase 1;Peptidase family M3","protein_coding" "AFR94448","No alias","Cryptococcus neoformans","hypothetical protein;Peptidase family M48","protein_coding" "AFR94766","No alias","Cryptococcus neoformans","STE24 endopeptidase;Peptidase family M48;CAAX prenyl protease N-terminal, five membrane helices","protein_coding" "AFR95622","No alias","Cryptococcus neoformans","mitochondrial inner membrane protease ATP23;Peptidase M76 family","protein_coding" "AFR96060","No alias","Cryptococcus neoformans","hypothetical protein;Peptidase family M50","protein_coding" "AFR97005","No alias","Cryptococcus neoformans","metalloendopeptidase;Peptidase family M48","protein_coding" "AFR97484","No alias","Cryptococcus neoformans","extracellular elastinolytic metalloproteinase;Fungalysin metallopeptidase (M36);Fungalysin/Thermolysin Propeptide Motif","protein_coding" "AFR97722","No alias","Cryptococcus neoformans","mitochondrial metalloendopeptidase OMA1;Peptidase family M48","protein_coding" "AFR97892","No alias","Cryptococcus neoformans","ATP-dependent metalloprotease;ATPase family associated with various cellular activities (AAA);AAA+ lid domain;Peptidase family M41","protein_coding" "AOA65425","No alias","Komagataella phaffii","Peptidase M3A/M3B catalytic domain","protein_coding" "AOA65486","No alias","Komagataella phaffii","ATPase, AAA-type, core","protein_coding" "AOA67013","No alias","Komagataella phaffii","Peptidase M48","protein_coding" "AOA67399","No alias","Komagataella phaffii","Peptidase M48","protein_coding" "AOA68057","No alias","Komagataella phaffii","Peptidase M3A/M3B catalytic domain","protein_coding" "AOA69221","No alias","Komagataella phaffii","Peptidase M76, ATP23","protein_coding" "AOA69461","No alias","Komagataella phaffii","Peptidase M41","protein_coding" "AOA69808","No alias","Komagataella phaffii","AAA ATPase, AAA+ lid domain","protein_coding" "AOA69809","No alias","Komagataella phaffii","AAA ATPase, AAA+ lid domain","protein_coding" "AOA69810","No alias","Komagataella phaffii","AAA ATPase, AAA+ lid domain","protein_coding" "AOA69811","No alias","Komagataella phaffii","AAA ATPase, AAA+ lid domain","protein_coding" "CAG77936","No alias","Yarrowia lipolytica","Peptidase M3A/M3B catalytic domain","protein_coding" "CAG78036","No alias","Yarrowia lipolytica","Peptidase M48","protein_coding" "CAG78066","No alias","Yarrowia lipolytica","Peptidase M76, ATP23","protein_coding" "CAG78076","No alias","Yarrowia lipolytica","Peptidase M48","protein_coding" "CAG78497","No alias","Yarrowia lipolytica","Peptidase M3A/M3B catalytic domain","protein_coding" "CAG82601","No alias","Yarrowia lipolytica","Peptidase M41","protein_coding" "CAG82648","No alias","Yarrowia lipolytica","Peptidase M41","protein_coding" "CAG83853","No alias","Yarrowia lipolytica","Peptidase M3A/M3B catalytic domain","protein_coding" "CAG83880","No alias","Yarrowia lipolytica","ATPase, AAA-type, core","protein_coding" "CAK38759","No alias","Aspergillus niger","ATPase family associated with various cellular activities (AAA)","protein_coding" "CAK39271","No alias","Aspergillus niger","Peptidase family M3","protein_coding" "CAK39542","No alias","Aspergillus niger","FtsH Extracellular","protein_coding" "CAK40728","No alias","Aspergillus niger","Peptidase family M3","protein_coding" "CAK42332","No alias","Aspergillus niger","Peptidase family M3","protein_coding" "CAK44738","No alias","Aspergillus niger","Peptidase family M48","protein_coding" "CAK44831","No alias","Aspergillus niger","Peptidase M76 family","protein_coding" "CAK46297","No alias","Aspergillus niger","Thermolysin metallopeptidase, alpha-helical domain","protein_coding" "CAK48098","No alias","Aspergillus niger","Peptidase family M3","protein_coding" "CAL00682","No alias","Aspergillus niger","Peptidase family M48","protein_coding" "CBF73605","No alias","Aspergillus nidulans","penicillolysin/deuterolysin metalloprotease, putative","protein_coding" "CBF75008","No alias","Aspergillus nidulans","hypothetical protein","protein_coding" "CBF77262","No alias","Aspergillus nidulans","mitochondrial inner membrane AAA protease Yta12, putative","protein_coding" "CBF77446","No alias","Aspergillus nidulans","CaaX prenyl protease","protein_coding" "CBF80285","No alias","Aspergillus nidulans","metalloproteinase, putative","protein_coding" "CBF81608","No alias","Aspergillus nidulans","intermembrane space AAA protease IAP-1","protein_coding" "CBF82799","No alias","Aspergillus nidulans","hypothetical protein","protein_coding" "CBF83425","No alias","Aspergillus nidulans","endothelin-converting enzyme","protein_coding" "CBF85685","No alias","Aspergillus nidulans","mitochondrial inner membrane metallopeptidase Oma1, putative","protein_coding" "EAA26824","No alias","Neurospora crassa","Peptidase M35, deuterolysin","protein_coding" "EAA27232","No alias","Neurospora crassa","ATPase, AAA-type, core","protein_coding" "EAA27520","No alias","Neurospora crassa","AAA ATPase, AAA+ lid domain","protein_coding" "EAA27995","No alias","Neurospora crassa","Peptidase M76, ATP23","protein_coding" "EAA28872","No alias","Neurospora crassa","Lysine-specific metallo-endopeptidase","protein_coding" "EAA30495","No alias","Neurospora crassa","Peptidase M4, C-terminal","protein_coding" "EAA32128","No alias","Neurospora crassa","Peptidase M48","protein_coding" "EAA32417","No alias","Neurospora crassa","Peptidase M48","protein_coding" "EAA33124","No alias","Neurospora crassa","Peptidase M3A/M3B catalytic domain","protein_coding" "EAA34783","No alias","Neurospora crassa","Peptidase M3A/M3B catalytic domain","protein_coding" "EAL84418","No alias","Aspergillus fumigatus","metalloproteinase, putative","protein_coding" "EAL85468","No alias","Aspergillus fumigatus","elastinolytic metalloproteinase Mep","protein_coding" "EAL86879","No alias","Aspergillus fumigatus","metallopeptidase MepB","protein_coding" "EAL87365","No alias","Aspergillus fumigatus","mitochondrial inner membrane AAA protease Yta12, putative","protein_coding" "EAL88715","No alias","Aspergillus fumigatus","metallopeptidase Mip1","protein_coding" "EAL89418","No alias","Aspergillus fumigatus","penicillolysin/deuterolysin metalloprotease, putative","protein_coding" "EAL89639","No alias","Aspergillus fumigatus","intermembrane space AAA protease IAP-1","protein_coding" "EAL89815","No alias","Aspergillus fumigatus","mitochondrial inner membrane metallopeptidase Oma1, putative","protein_coding" "EAL90028","No alias","Aspergillus fumigatus","CaaX prenyl protease Ste24","protein_coding" "EAL92341","No alias","Aspergillus fumigatus","endothelin-converting enzyme","protein_coding" "EAL93054","No alias","Aspergillus fumigatus","Ku70-binding protein, putative","protein_coding" "EAL94106","No alias","Aspergillus fumigatus","metalloproteinase, putative","protein_coding" "EAU81629","No alias","Coprinopsis cinerea","peptidase M48 family protein","protein_coding" "EAU82511","No alias","Coprinopsis cinerea","metalloprotease MEP2","protein_coding" "EAU82657","No alias","Coprinopsis cinerea","Peptidase M35, deuterolysin","protein_coding" "EAU82683","No alias","Coprinopsis cinerea","Lysine-specific metallo-endopeptidase","protein_coding" "EAU82952","No alias","Coprinopsis cinerea","Peptidase M36, fungalysin","protein_coding" "EAU82955","No alias","Coprinopsis cinerea","extracellular elastinolytic metalloproteinase","protein_coding" "EAU82961","No alias","Coprinopsis cinerea","metalloproteinase 10","protein_coding" "EAU83492","No alias","Coprinopsis cinerea","metalloendopeptidase","protein_coding" "EAU83617","No alias","Coprinopsis cinerea","extracellular elastinolytic metalloproteinase","protein_coding" "EAU85481","No alias","Coprinopsis cinerea","Peptidase M48","protein_coding" "EAU86243","No alias","Coprinopsis cinerea","metallopeptidase MepB","protein_coding" "EAU86365","No alias","Coprinopsis cinerea","metalloprotease","protein_coding" "EAU86463","No alias","Coprinopsis cinerea","metalloprotease","protein_coding" "EAU88544","No alias","Coprinopsis cinerea","ATP-dependent peptidase","protein_coding" "EAU92673","No alias","Coprinopsis cinerea","Peptidase M41AAA ATPase, AAA+ lid domainATPase, AAA-type, corePeptidase M41, FtsH extracellular","protein_coding" "EAU92790","No alias","Coprinopsis cinerea","mitochondrial intermediate peptidase","protein_coding" "EDN91150","No alias","Sclerotinia sclerotiorum","Peptidase M41","protein_coding" "EDN96370","No alias","Sclerotinia sclerotiorum","Peptidase M3A/M3B catalytic domain","protein_coding" "EDN98882","No alias","Sclerotinia sclerotiorum","Peptidase M35, deuterolysin","protein_coding" "EDO02604","No alias","Sclerotinia sclerotiorum","Peptidase M48","protein_coding" "EDO03217","No alias","Sclerotinia sclerotiorum","Peptidase M13, C-terminal domain","protein_coding" "EDO03609","No alias","Sclerotinia sclerotiorum","Peptidase M41","protein_coding" "EDO03613","No alias","Sclerotinia sclerotiorum","CAAX prenyl protease 1, N-terminal","protein_coding" "EED45749","No alias","Aspergillus flavus","neutral protease 2 precursor, putative","protein_coding" "EED48216","No alias","Aspergillus flavus","extracellular elastinolytic metalloproteinase, putative","protein_coding" "EED48367","No alias","Aspergillus flavus","metalloproteinase, putative","protein_coding" "EED48421","No alias","Aspergillus flavus","conserved hypothetical protein","protein_coding" "EED48603","No alias","Aspergillus flavus","metallopeptidase Mip1","protein_coding" "EED49597","No alias","Aspergillus flavus","matrix metalloproteinase, putative","protein_coding" "EED49723","No alias","Aspergillus flavus","penicillolysin/deuterolysin metalloprotease, putative","protein_coding" "EED50577","No alias","Aspergillus flavus","mitochondrial inner membrane AAA protease Yta12, putative","protein_coding" "EED51012","No alias","Aspergillus flavus","thimet oligopeptidase, putative","protein_coding" "EED51504","No alias","Aspergillus flavus","neutral protease 2 precursor, putative","protein_coding" "EED52152","No alias","Aspergillus flavus","elastinolytic metalloproteinase Mep","protein_coding" "EED53027","No alias","Aspergillus flavus","Ku70-binding protein, putative","protein_coding" "EED53849","No alias","Aspergillus flavus","CaaX prenyl protease Ste24","protein_coding" "EED55302","No alias","Aspergillus flavus","mitochondrial inner membrane metallopeptidase Oma1, putative","protein_coding" "EED55480","No alias","Aspergillus flavus","intermembrane space AAA protease IAP-1","protein_coding" "EED56994","No alias","Aspergillus flavus","metallopeptidase MepB","protein_coding" "EED57052","No alias","Aspergillus flavus","thimet oligopeptidase, putative","protein_coding" "EED57282","No alias","Aspergillus flavus","endothelin-converting enzyme","protein_coding" "EED57889","No alias","Aspergillus flavus","conserved hypothetical protein","protein_coding" "EED79121","No alias","Postia placenta","Peptidase M3A/M3B catalytic domain","protein_coding" "EED82152","No alias","Postia placenta","Peptidase M48","protein_coding" "EED82275","No alias","Postia placenta","Peptidase M3A/M3B catalytic domain","protein_coding" "EED85251","No alias","Postia placenta","Peptidase M3A/M3B catalytic domain","protein_coding" "EFI28231","No alias","Coprinopsis cinerea","metalloprotease","protein_coding" "EFI28400","No alias","Coprinopsis cinerea","endothelin-converting enzyme 1","protein_coding" "EFI28753","No alias","Coprinopsis cinerea","metalloprotease ATP23","protein_coding" "EGR44217","No alias","Trichoderma reesei","FTP domain","protein_coding" "EGR45489","No alias","Trichoderma reesei","H-type lectin domain","protein_coding" "EGR46772","No alias","Trichoderma reesei","Peptidase M3A/M3B catalytic domain","protein_coding" "EGR46844","No alias","Trichoderma reesei","Peptidase M4, C-terminal","protein_coding" "EGR47708","No alias","Trichoderma reesei","Peptidase M48","protein_coding" "EGR47931","No alias","Trichoderma reesei","Peptidase M41","protein_coding" "EGR49232","No alias","Trichoderma reesei","Peptidase M35, deuterolysin","protein_coding" "EGR49342","No alias","Trichoderma reesei","CAAX prenyl protease 1, N-terminal","protein_coding" "EGR49888","No alias","Trichoderma reesei","Protealysin, N-terminal propeptide","protein_coding" "EGR50222","No alias","Trichoderma reesei","Peptidase M3A/M3B catalytic domain","protein_coding" "EGR52283","No alias","Trichoderma reesei","Peptidase M76, ATP23","protein_coding" "EGR52562","No alias","Trichoderma reesei","Peptidase M41","protein_coding" "EJF58150","No alias","Dichomitus squalens","Fungalysin metallopeptidase (M36)","protein_coding" "EJF58984","No alias","Dichomitus squalens","Lysine-specific metallo-endopeptidase","protein_coding" "EJF58987","No alias","Dichomitus squalens","Lysine-specific metallo-endopeptidase","protein_coding" "EJF60844","No alias","Dichomitus squalens","Fungalysin metallopeptidase (M36)","protein_coding" "EJF60883","No alias","Dichomitus squalens","Peptidase family M48","protein_coding" "EJF60891","No alias","Dichomitus squalens","Fungalysin/Thermolysin Propeptide Motif","protein_coding" "EJF60895","No alias","Dichomitus squalens","Fungalysin/Thermolysin Propeptide Motif","protein_coding" "EJF60896","No alias","Dichomitus squalens","Fungalysin/Thermolysin Propeptide Motif","protein_coding" "EJF60897","No alias","Dichomitus squalens","Fungalysin/Thermolysin Propeptide Motif","protein_coding" "EJF62033","No alias","Dichomitus squalens","Peptidase family M48","protein_coding" "ESU06799","No alias","Fusarium graminearum","cell division protease ftsH","protein_coding" "ESU08229","No alias","Fusarium graminearum","Peptidase M13, N-terminal domain","protein_coding" "ESU09749","No alias","Fusarium graminearum","extracellular elastinolytic metalloproteinase precursor","protein_coding" "ESU11171","No alias","Fusarium graminearum","Peptidase M3A/M3B catalytic domain","protein_coding" "ESU11933","No alias","Fusarium graminearum","Peptidase M48","protein_coding" "ESU12963","No alias","Fusarium graminearum","ATPase, AAA-type, core","protein_coding" "ESU13015","No alias","Fusarium graminearum","Peptidase M3A/M3B catalytic domain","protein_coding" "ESU13130","No alias","Fusarium graminearum","Peptidase M76, ATP23","protein_coding" "ESU15079","No alias","Fusarium graminearum","Peptidase M35, deuterolysin","protein_coding" "ESU15185","No alias","Fusarium graminearum","H-type lectin domain","protein_coding" "ESU15304","No alias","Fusarium graminearum","Peptidase M4 domain","protein_coding" "ESU15746","No alias","Fusarium graminearum","Peptidase M3A/M3B catalytic domain","protein_coding" "ESU15844","No alias","Fusarium graminearum","Protealysin, N-terminal propeptide","protein_coding" "ESU16878","No alias","Fusarium graminearum","Peptidase M48","protein_coding" "ESU17612","No alias","Fusarium graminearum","Peptidase M3A/M3B catalytic domain","protein_coding" "KHC73186","No alias","Candida albicans","mitochondrial intermediate peptidase;Peptidase family M3","protein_coding" "KHC76546","No alias","Candida albicans","hypothetical protein;Peptidase family M48","protein_coding" "KHC76643","No alias","Candida albicans","ATP-dependent metallopeptidase HflB;ATPase family associated with various cellular activities (AAA);AAA+ lid domain;Peptidase family M41","protein_coding" "KHC77979","No alias","Candida albicans","STE24 endopeptidase;"CAAX prenyl protease N-terminal, five membrane helices";Peptidase family M48","protein_coding" "KHC80121","No alias","Candida albicans","ATP-dependent metallopeptidase HflB;ATPase family associated with various cellular activities (AAA);AAA+ lid domain;Peptidase family M41","protein_coding" "KHC81146","No alias","Candida albicans","ATP-dependent metallopeptidase HflB;FtsH Extracellular;AAA+ lid domain;ATPase family associated with various cellular activities (AAA);Peptidase family M41","protein_coding" "KHC81728","No alias","Candida albicans","mitochondrial inner membrane protease ATP23;Peptidase M76 family","protein_coding" "KHC83305","No alias","Candida albicans","saccharolysin;Peptidase family M3","protein_coding" "MGG_00480T0","No alias","Pyricularia oryzae","Mitochondrial inner membrane protease ATP23 [Source:UniProtKB/Swiss-Prot;Acc:A4RF31]","protein_coding" "MGG_00487T0","No alias","Pyricularia oryzae","Mitochondrial intermediate peptidase [Source:UniProtKB/Swiss-Prot;Acc:A4RF25]","protein_coding" "MGG_03029T0","No alias","Pyricularia oryzae","Metalloproteinase [Source:UniProtKB/TrEMBL;Acc:G5EHM4]","protein_coding" "MGG_03808T0","No alias","Pyricularia oryzae","Putative uncharacterized protein [Source:UniProtKB/TrEMBL;Acc:G4NHL0]","protein_coding" "MGG_03926T0","No alias","Pyricularia oryzae","Cell division protease ftsH [Source:UniProtKB/TrEMBL;Acc:G4NH61]","protein_coding" "MGG_04858T0","No alias","Pyricularia oryzae","Metallopeptidase MepB [Source:UniProtKB/TrEMBL;Acc:G4N2B8]","protein_coding" "MGG_05878T0","No alias","Pyricularia oryzae","Extracellular metalloprotease [Source:UniProtKB/TrEMBL;Acc:G4N3X7]","protein_coding" "MGG_06643T0","No alias","Pyricularia oryzae","Putative uncharacterized protein [Source:UniProtKB/TrEMBL;Acc:G4MKP3]","protein_coding" "MGG_06951T0","No alias","Pyricularia oryzae","CAAX prenyl protease 1 [Source:UniProtKB/TrEMBL;Acc:G4MNG8]","protein_coding" "MGG_07038T0","No alias","Pyricularia oryzae","Putative uncharacterized protein [Source:UniProtKB/TrEMBL;Acc:G4MZP8]","protein_coding" "MGG_07052T0","No alias","Pyricularia oryzae","Mitochondrial metalloendopeptidase OMA1 [Source:UniProtKB/TrEMBL;Acc:G4MZR0]","protein_coding" "MGG_07441T0","No alias","Pyricularia oryzae","Paraplegin [Source:UniProtKB/TrEMBL;Acc:G4N151]","protein_coding" "MGG_09617T0","No alias","Pyricularia oryzae","Putative uncharacterized protein [Source:UniProtKB/TrEMBL;Acc:G4NL84]","protein_coding" "MGG_10015T0","No alias","Pyricularia oryzae","Putative uncharacterized protein [Source:UniProtKB/TrEMBL;Acc:G4N9C9]","protein_coding" "MGG_10927T0","No alias","Pyricularia oryzae","Neutral protease 2 homolog MGG_10927 [Source:UniProtKB/Swiss-Prot;Acc:Q2KH28]","protein_coding" "MGG_13252T0","No alias","Pyricularia oryzae","Extracellular metalloproteinase MEP [Source:UniProtKB/Swiss-Prot;Acc:A4QWP8]","protein_coding" "MGG_14981T0","No alias","Pyricularia oryzae","hypothetical protein [Source:BROAD_Magnaporthe_DB;Acc:MGG_14981]","protein_coding" "MGG_15370T0","No alias","Pyricularia oryzae","Metalloproteinase [Source:UniProtKB/TrEMBL;Acc:G4NFY3]","protein_coding" "MGG_16546T0","No alias","Pyricularia oryzae","Putative uncharacterized protein [Source:UniProtKB/TrEMBL;Acc:G4MLH1]","protein_coding" "MGG_16938T0","No alias","Pyricularia oryzae","Putative uncharacterized protein [Source:UniProtKB/TrEMBL;Acc:G4N1G9]","protein_coding" "MGG_17758T0","No alias","Pyricularia oryzae","Putative uncharacterized protein [Source:UniProtKB/TrEMBL;Acc:G4NHM9]","protein_coding" "POW03513","No alias","Puccinia striiformis","Peptidase M36, fungalysin","protein_coding" "POW04719","No alias","Puccinia striiformis","Peptidase M3A/M3B catalytic domain","protein_coding" "POW05088","No alias","Puccinia striiformis","CAAX prenyl protease 1, N-terminal;Peptidase M48","protein_coding" "POW11900","No alias","Puccinia striiformis","AAA ATPase, AAA+ lid domain;ATPase, AAA-type, core;Peptidase M41","protein_coding" "POW12480","No alias","Puccinia striiformis","Peptidase M48","protein_coding" "POW16981","No alias","Puccinia striiformis","Peptidase M76, ATP23","protein_coding" "POW17653","No alias","Puccinia striiformis","Peptidase M48","protein_coding" "SPAC1F3.10c.1","No alias","Schizosaccharomyces pombe","mitochondrial intermediate peptidase Oct1 (predicted) [Source:PomBase;Acc:SPAC1F3.10c]","protein_coding" "SPAC3H1.05.1","No alias","Schizosaccharomyces pombe","CAAX prenyl protease (predicted) [Source:PomBase;Acc:SPAC3H1.05]","protein_coding" "SPAP14E8.04.1","No alias","Schizosaccharomyces pombe","metallopeptidase Oma1 (predicted) [Source:PomBase;Acc:SPAP14E8.04]","protein_coding" "SPBC543.09.1","No alias","Schizosaccharomyces pombe","mitochondrial m-AAA protease Yta12 (predicted) [Source:PomBase;Acc:SPBC543.09]","protein_coding" "SPCC320.12.1","No alias","Schizosaccharomyces pombe","mitochondrial inner membrane peptidase Atp23 (predicted) [Source:PomBase;Acc:SPCC320.12]","protein_coding" "SPCC965.04c.1","No alias","Schizosaccharomyces pombe","mitochondrial inner membrane i-AAA protease complex subunit Yme1 (predicted) [Source:PomBase;Acc:SPCC965.04c]","protein_coding" "YCL057W","No alias","Saccharomyces cerevisiae","Zinc metalloendopeptidase; found in the cytoplasm and intermembrane space of mitochondria; with Cym1p, involved in degradation of mitochondrial proteins and of presequence peptides cleaved from imported proteins; protein abundance increases in response to DNA replication stress [Source:SGD;Acc:S000000562]","protein_coding" "YER017C","No alias","Saccharomyces cerevisiae","Mitochondrial inner membrane m-AAA protease component; mediates degradation of misfolded or unassembled proteins; also required for correct assembly of mitochondrial enzyme complexes; involved in cytoplasmic mRNA translation and aging; expression of human homolog AFG3L2 can complement yeast yta12 afg3 double mutant [Source:SGD;Acc:S000000819]","protein_coding" "YJR117W","No alias","Saccharomyces cerevisiae","Highly conserved zinc metalloprotease; functions in two steps of a-factor maturation, C-terminal CAAX proteolysis and the first step of N-terminal proteolytic processing; cleaves both isoprenylated and non-prenylated oligopeptides; contains multiple transmembrane spans; human homolog ZMPSTE24 implicated in mandibuloacral dysplasia (MAD), and can complement yeast null mutant [Source:SGD;Acc:S000003878]","protein_coding" "YKL134C","No alias","Saccharomyces cerevisiae","Mitochondrial intermediate peptidase; cleaves destabilizing N-terminal residues of a subset of proteins upon import, after their cleavage by mitochondrial processing peptidase (Mas1p-Mas2p); may contribute to mitochondrial iron homeostasis [Source:SGD;Acc:S000001617]","protein_coding" "YKR087C","No alias","Saccharomyces cerevisiae","Metalloendopeptidase of the mitochondrial inner membrane; important for adaptive responses to various homeostatic insults, preservation of normal mitochondrial function under damage-eliciting conditions, and stability of respiratory supercomplexes; involved in turnover of membrane-embedded proteins; mediates degradation of Cox1p in coa2 mutant cells; zebrafish ortholog has a role in organ development and mouse ortholog is also required for respiratory supercomplex stability [Source:SGD;Acc:S000001795]","protein_coding" "YMR089C","No alias","Saccharomyces cerevisiae","Mitochondrial inner membrane m-AAA protease component; mediates degradation of misfolded or unassembled proteins; also required for correct assembly of mitochondrial enzyme complexes; overexpression of human AFG3L2 complements respiratory defect of yeast afg3 yta12 double null mutation, but overexpression of disease-associated AFG3L2 variants does not; expression of both human SPG7 (paraplegin) and AFG3L2 complements yeast yta12 afg3 double mutation [Source:SGD;Acc:S000004695]","protein_coding" "YNR020C","No alias","Saccharomyces cerevisiae","Putative metalloprotease of the mitochondrial inner membrane; required for processing of Atp6p; has an additional role in assembly of the F0 sector of the F1F0 ATP synthase complex; substrate of the Mia40p-Erv1p disulfide relay system, and folding is assisted by Mia40p [Source:SGD;Acc:S000005303]","protein_coding" "YPR024W","No alias","Saccharomyces cerevisiae","Catalytic subunit of i-AAA protease complex; complex is located in mitochondrial inner membrane; responsible for degradation of unfolded or misfolded mitochondrial gene products; serves as nonconventional translocation motor to pull PNPase into intermembrane space; also has role in intermembrane space protein folding; mutation causes elevated rate of mitochondrial turnover; human homolog YME1L1 can complement yeast null mutant [Source:SGD;Acc:S000006228]","protein_coding"